English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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Systemic manifestations are progressive and may lead to serious complications: SJR uses a similar algorithm as the Google page rank; it provides enfemedad quantitative and qualitative measure of the journal’s impact.
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Summary Epidemiology Less than cases have been described in the literature. Clinical description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities. As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory. Read this article in English. Diagnostic methods Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic.
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No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has been tested successfully in one case with intestinal and CNS manifestations.
Term Bank – enfermedad de degos – Spanish English Dictionary
MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities. Are you a health professional able to prescribe or dispense drugs? The documents contained in this web site are presented for information purposes only.
Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Ocular involvement, which affects the eyelids, conjuctiva, retina, sclera and the choroid plexus, as well as the development of diplopia and ophthalmoplegia as secondary side effects of the neurologic involvementhas also been described.
A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, in order to assess the long-term prognosis.
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For all other comments, please send your remarks via contact us. Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases. Previous article Next article. The etiopathogenesis of the disease remains unknown. Face, scalp, palms of hands and soles of feet are rarely involved.
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This item has received. Later a wedge-shaped connective ed necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs. Over several days, the center of the lesions sinks and develops a characteristic morphology: Prognosis Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions.
This condition is chronic and lesions persist over years, often throughout life. It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting as pleuritis. Dehos The etiopathogenesis of the disease remains unknown. Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic.
Enfermedad de Degos
Check this box if you wish to receive a copy of your message. All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style. Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed.
The histology of early lesions resembles cutaneous lupus erythematosus see this term. To improve our enfermedae and products, we use “cookies” own or third parties authorized to show advertising xe to client preferences through the analyses of navigation customer behavior.